WebJan 14, 2011 · Trimethyllysine dioxygenase (EC 1.14.11.8) Cite Download Contents 1 Names and Identifiers 2 Pathways 3 Biochemical Reactions 4 Catalytic Activity 5 … WebJan 14, 2011 · trimethyllysine dioxygenase Synonyms ε -trimethyllysine 2-oxoglutarate dioxygenase oxygenase, trimethyllysine di- TML dioxygenase TML hydroxylase TML- α -ketoglutarate dioxygenase TMLD trimethyllysine α -ketoglutarate dioxygenase CAS registry number 84012-77-1 Keywords Molecular Weight Analytical Chemistry Reaction Type …
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WebApr 10, 2024 · The first step in carnitine biosynthesis is catalyzed by trimethyllysine hydroxylase (TMLH), a non-heme Fe (II) and 2-oxoglutarate (2OG)-dependent oxygenase, … WebSep 6, 2024 · Only trimethyllysine dioxygenase (TMLD) and γ-butyrobetaine dioxygenase (BBD) deficiencies have been reported; both are denoted with asterisks. ( b) Carnitine transport and mitochondrial carnitine–acylcarnitine cycle. craftsman snowblower engine parts
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WebApr 25, 2024 · A 100mM solution of dithiotreitol (DTT) was added and incubated at 30 °C for 1 h, then alkylated with sufficient iodoacetamide (IAM) for 1 h at room temperature. Add 25 mM ammonium bicarbonate buffer and dilute 4 times. Trypsin (trypsin: protein = 1:50) was added and incubated overnight at 37℃. WebProtein target information for Trimethyllysine dioxygenase, mitochondrial (human). Find diseases associated with this biological target and compounds tested against it in … WebMar 6, 2013 · During this multi-step process, N 6-trimethyllysine is converted into 3-hydroxy-N 6-trimethyllysine by trimethyllysine dioxygenase (EC 1.14.11.8) in the presence of α-KG. γ-butyrobetaine dioxygenase [EC 1.14.11.1] and betaine-aldehyde dehydrogenase (EC 1.2.1.8) are severely impeded by the Al challenge imposed on astrocytes and hepatocytes ... craftsman snow blower electric start